缩窄性心包炎CT病例影像诊断分析(图文)

2019-02-15 佚名 影像园

女,60岁,气促、心悸16年,腹胀、伴双下肢浮肿1年,加重1月。

【病史临床

女,60岁,气促、心悸16年,腹胀、伴双下肢浮肿1年,加重1月。

【影像图片】 






胸部CT平扫纵隔窗不同层面(图A、B、C)

【影像表现】 

沿心包可见弧形高密度影包绕,CT值大约200HU左右,与心腔等软组织密度形成鲜明对比。右侧胸腔内还可见大量液性密度影,CT值大约20HU左右。

诊断

缩窄性心包炎(行心包剥离术证实)

【鉴别诊断】 

1.冠状动脉粥样硬化性心脏病;2.肥厚性心肌病;3.缩窄性心包炎

【讨论】 

心包疾病长期不愈或心包积液吸收不彻底,可引起心包肥厚、粘连,后期钙化包绕心脏,形成缩窄性心包炎,从而限制了心脏活动导致心脏舒张功能受限,产生一系列体循环及肺循环回流受限的表现。心脏舒张功能异常表现有右心室受压,舒张受限,静脉血回流入右心室受阻,上下腔静脉扩张、肝大、腹水等。左心室受压,舒张期进入左心室的血少,排出也少进而脉压下降,二尖瓣口被纤维包绕时,可引起肺循环淤血,左房增大,出现症状如心悸、气短、咳嗽、颈静脉怒张、腹胀、肝大、腹水等。

影像诊断要点 CT上主要征象表现为心包增厚约5~20mm,多呈弥漫性,也可局部增厚,后期心包可出现多少不等的钙化,严重呈弧形、蛋壳状,形成“盔甲心”。由于体静脉压力升高,还可见上下腔静脉扩张,肝大及胸腹腔积液等体静脉淤血的表现,心包钙化对缩窄性心包炎的诊断很重要,一般观察到心包钙化是缩窄性心包炎的确诊,但必须注意个别病例可能有心包钙化而无心包缩窄的功能改变,因此必须结合临床及其他征象,另外,心包钙化并不是诊断缩窄性心包炎的必要征像,很多病例并没有继发的心包钙化。GRE序列电影MRI示心室壁运动幅度降低,特别于舒张期明显。M型超声心动图示心包增厚,其回声增强,增厚极不均匀。室壁舒张中晚期活动受限,双心房扩大,心室腔正常或减小。下腔静脉扩张。
  
CT对于显示心包增厚及钙化灶具有明显的优势,但不能动态显示心脏舒张受限的情况。GRE序列电影MRI能动态显示心脏功能变化,为最佳影像学诊断方法,但缺点在于程序复杂,价格昂贵,而超声心动图可动态显示心脏活动受限的征象,超声多普勒可显示血流变化情况,应作为首选的影像学方法。本病的确诊需要临床、及影像学等紧密结合进行综合诊断。

【问题】
 
True OR False
1.心包周围高密度环形影为出血表现; 对: 错
2.心包钙化并伴有大量心包积液; 对: 错
3.伴有右侧胸腔积液; 对: 错
4.心包周围环形包绕心脏的高密度影为心包钙化。 对: 错

正确答案: 1:× 2:× 3:√ 4:√

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